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KMID : 1040620150210020175
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Clinical and Molecular Hepatology
2015 Volume.21 No. 2 p.175 ~ p.179
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Caroli’s disease misdiagnosed as intraductal papillary neoplasm of the bile duct
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Gu Dae-Hoe
Park Min-Seon
Jung Chang-Ho
Yoo Yang-Jae
Cho Jae-Young
Lee Yun-Ho
Seo Yeon-Seok
Yim Hyung-Joon
Um Soon-Ho
Ryu Ho-Sang
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Abstract
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Caroli’s disease is a rare autosomal-recessive disorder caused by malformation of the ductal plate during embryonic development. Although it is present at birth, Caroli’s disease is typically not diagnosed until between the second and fourth decades of life, as it was in the present patient. Here we report a rare case of Caroli’s disease limited to one liver segment, which was initially misdiagnosed as an intraductal papillary neoplasm of the bile duct. The asymptomatic patient was treated with liver segmentectomy.
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KEYWORD
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Caroli’s disease, Intraductal papillary neoplasm of the bile duct, Segmentectomy
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